Tyrosine1000®
▶Nutritional supplement for the dietary management of inborn
errors of amino acid metabolism in adults and children from
birth.
POWDER, tyrosine 1 g, carbohydrate 2.9 g, fat nil, energy 63 kJ
(15kcal)/4-g sachet.
Tyrosine1000 oral powder 4g sachets(Vitaflo International Ltd)
30 sachet (ACBS).NHS indicative price = £ 5. 23
Valine50®
▶Nutritional supplement for the dietary management of inborn
errors of amino acid metabolism in adults and children from
birth.
POWDER, valine 50mg, carbohydrate 3.8 g, fat nil, energy 63 kJ
(15kcal)/4 g
Valine50 oral powder 4g sachets(Vitaflo International Ltd)
30 sachet (ACBS).NHS indicative price = £ 57. 14
Phenylketonuria
Add-Ins®
▶Nutritional supplement for the dietary management of proven
phenylketonuria in children over 4 years.
POWDER, protein equivalent (containing essential and non-
essential amino acids except phenylalanine) 10g, carbohydrate
nil, fat 5.1 g, energy 359 kJ (86 kcal)/18.2-g sachet, with
vitamins, minerals, and trace elements.
Add Ins oral powder 18.2g sachets(Nutricia Ltd)
60 sachet (ACBS).NHS indicative price = £ 394. 20
Easiphen®
▶Nutritional supplement for the dietary management of proven
phenylketonuria in children over 8 years.
LIQUID, protein equivalent (containing essential and non-
essential amino acids except phenylalanine) 6.7 g, carbohydrate
5.1 g, fat 2 g, energy 275 kJ (65kcal)/100mL with vitamins,
minerals, and trace elements.
Easiphen liquid(Nutricia Ltd)
250 ml (ACBS).NHS indicative price = £ 10. 12
L-Tyrosine
▶Nutritional supplement for the dietary management of
phenylketonuria in pregnant women with low plasma tyrosine
concentrations.
POWDER, L-tyrosine 20g, carbohydrate 76.8g, fat nil, energy
1612 kJ (379 kcal)/100g.
L-Tyrosine powder(Nutricia Ltd)
100 gram (ACBS).NHS indicative price = £ 22. 98
Lophlex®
▶Nutritional supplement for the dietary management of proven
phenylketonuria in children over 8 years and adults including
pregnant women.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine) 20 g, carbohydrate 2.5 g, fat 60mg,
fibre 220 mg, energy 385 kJ (91 kcal)/27.8-g sachet, with
vitamins, minerals, and trace elements.
Lophlex powder 27.8g sachets berry(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 303. 90
Lophlex powder 27.8g sachets orange(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 303. 90
Lophlex powder 27.8g sachets unflavoured(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 303. 90
Loprofin®PKU Drink
▶Nutritional supplement for the dietary management of
phenylketonuria in children over 1 year and adults.
LIQUID, protein (cows’milk) 400 mg (phenylalanine 10 mg),
lactose 9.4 g, fat 2 g, energy 165 kJ (40kcal)/100mL.
Loprofin PKU drink(Nutricia Ltd)
200 ml (ACBS).NHS indicative price = £ 0. 79
Loprofin®Sno-Pro
▶Nutritional supplement for the dietary management of
phenylketonuria, chronic renal failure and other inborn errors
of amino acid metabolism.
LIQUID, protein (cows’milk) 220 mg (phenylalanine 12.5 mg),
carbohydrate 8 g, fat 3.8 g, energy 273 kJ (65 kcal)/100mL.
Contains lactose.
Loprofin SNO-PRO drink(Nutricia Ltd)
200 ml (ACBS).NHS indicative price = £ 1. 31
Phlexy-10®Exchange System
▶Nutritional supplement for the dietary management of
phenylketonuria.
CAPSULES, protein equivalent (essential and non-essential
amino acids except phenylalanine) 416.5mg/capsule.
Phlexy-10 500mg capsules(Nutricia Ltd)
200 capsule (ACBS).NHS indicative price = £ 45. 49
TABLETS, protein equivalent (essential and non-essential amino
acids except phenylalanine) 833 mg tablet.
Phlexy-10 tablets(Nutricia Ltd)
75 tablet (ACBS).NHS indicative price = £ 29. 25
DRINK MIX, powder, protein equivalent (essential and non-
essential amino acids except phenylalanine) 8.33 g,
carbohydrate 8.8 g/20-g sachet.
Phlexy-10 drink mix apple & blackcurrant(Nutricia Ltd)
600 gram (ACBS).NHS indicative price = £ 134. 70
Phlexy-10 drink mix citrus burst(Nutricia Ltd)
600 gram (ACBS).NHS indicative price = £ 134. 70
Phlexy-10 drink mix tropical surprise(Nutricia Ltd)
600 gram (ACBS).NHS indicative price = £ 134. 70
Phlexy-Vits®
▶For use as a vitamin and mineral component of restricted
therapeutic diets in children over 11 years and adults with
phenylketonuria and similar amino acid abnormalities.
POWDER, vitamins, minerals, and trace elements
Phlexy-Vits powder(Nutricia Ltd)
210 gram (ACBS).NHS indicative price = £ 74. 70
TABLETS, vitamins, minerals, and trace elements
Phlexy-Vits tablets(Nutricia Ltd)
180 tablet (ACBS).NHS indicative price = £ 85. 60
PK Aid 4®
▶Nutritional supplement for the dietary management of
phenylketonuria in children and adults.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine) 79g, carbohydrate 4.5 g, fat nil,
energy 1420 kJ (334 kcal)/100g.
PK Aid 4 powder(Nutricia Ltd)
500 gram (ACBS).NHS indicative price = £ 149. 97
PKU Anamix®First Spoon
▶Nutritional supplement for the dietary management of proven
phenylketonuria in children from 6 months to 5 years.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine) 5g, carbohydrate 4.8 g, fat 150 mg,
fibre nil, energy 168 kJ (41 kcal)/12.5-g sachet, with vitamins,
minerals, and trace elements
PKU Anamix First Spoon oral powder 12.5g sachets(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 96. 30
PKU Anamix®Infant
▶Nutritional supplement for the dietary management of proven
phenylketonuria in children from birth to 3 years.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine) 13.1g, carbohydrate 49.5g, fat 23g,
fibre 5.3 g, energy 1915 kJ (457kcal)/100g, with vitamins,
minerals, and trace elements; standard dilution (15%) provides
protein equivalent 2g, carbohydrate 7.4 g, fat 3.5 g,fibre
800 mg, energy 287 kJ (69 kcal)/100mL
PKU Anamix Infant powder(Nutricia Ltd)
400 gram (ACBS).NHS indicative price = £ 37. 08
PKU Anamix®Junior
▶Nutritional supplement for the dietary management of
phenylketonuria in children 1–10 years.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine) 8.4 g, carbohydrate 9.9 g, fat 3.9 g,BNFC 2018 – 2019 Nutritional supplements for metabolic diseases 1049
Borderline substances|Appendix 2A2