CYSTIC RENAL DISEASES
Renal cyst is an isolated segment of the nephron which is dilated to
a diameter of 200 um or more. Cystic kidney is a kidney containing 3 or
more cysts.
• Classification of renal cystic diseases ...............................
I. Polycystic kidney disease.• Autosomal dominant polycystic kidney diseases ..................
- Autosomal recessive polycystic kidney disease.
II. Renal Medullary cysts. - Medullary cystic disease • Medullary sponge kidney
- Juvenile Nephronopthisis
III. Acquired renal cystic disease
IV. Renal cyst in hereditary syndrome - Tuberous sclerosis • Von Hippel-Lindau disease
- Others
V. Simple renal cyst - Single • Multiple
AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY
DISEASE (ADPKD)
It is one of the most common genetic disorders and is responsible
for approximately 10% of patients with end stage renal failure. It affects
1:400-1:1000 of people allover the world.