PKU Lophlex LQ 20 liquid orange(Nutricia Ltd)
125 ml (ACBS).NHS indicative price = £ 10. 83
PKU Lophlex®Sensation 20
▶Nutritional supplement for the dietary management of
phenylketonuria in children over 4 years and adults including
pregnant women.
SEMI-SOLID, protein equivalent (containing essential and non-
essential amino acids except phenylalanine) 20g, carbohydrate
20.2g,fibre 1 g, energy 706 kJ (166kcal)/109g, with vitamins,
minerals, and trace elements.
PKU Lophlex Sensation 20 berries(Nutricia Ltd)
327 gram (ACBS).NHS indicative price = £ 34. 59
PKU squeezie®
▶Nutritional supplement for the dietary management of
phenylketonuria in children from 6 months to 10 years.
LIQUID, protein equivalent (essential and non-essential amino
acids except phenylalanine) 10 g, carbohydrate 22.5 g, fat
500 mg, energy 565 kJ (135kcal)/85g, with vitamins, minerals,
and trace elements.
PKU squeezie liquid(Vitaflo International Ltd)
2550 gram (ACBS).NHS indicative price = £ 140. 04
PKU Maxamum®
▶Nutritional supplement for the dietary management of
phenylketonuria in children over 8 years and adults.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine) 39 g, carbohydrate 34 g, fat less
than 500 mg, energy 1260 kJ (297 kcal)/100g, with vitamins,
minerals, and trace elements.
PKU Maxamum oral powder 50g sachets orange(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 282. 60
PKU Maxamum oral powder 50g sachets unflavoured(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 282. 60
PKU Maxamum powder orange(Nutricia Ltd)
500 gram (ACBS).NHS indicative price = £ 94. 24
PKU Maxamum powder unflavoured(Nutricia Ltd)
500 gram (ACBS).NHS indicative price = £ 94. 24
Tyrosinaemia
Methionine-free TYR Anamix®Infant
▶Nutritional supplement for the dietary management of proven
tyrosinaemia type 1 in children from birth to 3 years.
POWDER, protein equivalent (essential and non-essential amino
acids except methionine, phenylalanine, and tyrosine) 13.1g,
carbohydrate 49.5 g, fat 23g,fibre 5.3 g, energy 1915 kJ
(457kcal)/100g, with vitamins, minerals, and trace elements;
standard dilution (15%) provides protein equivalent 2 g,
carbohydrate 7.4 g, fat 3.5 g,fibre 800 mg, energy 287 kJ
(69kcal)/100 mL.
TYR Anamix Infant methionine free powder(Nutricia Ltd)
400 gram (ACBS).NHS indicative price = £ 40. 79
TYR Anamix®Infant
▶Nutritional supplement for the dietary management of proven
tyrosinaemia where plasma-methionine concentrations are
normal in children from birth to 3 years.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine and tyrosine) 13.1g, carbohydrate
49.5g, fat 23g,fibre 5.3 g, energy 1915 kJ (457 kcal)/100g, with
vitamins, minerals, and trace elements; standard dilution (15%)
provides protein equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g,
fibre 800 mg, energy 287 kJ (69 kcal)/100mL.
TYR Anamix Infant methionine free powder(Nutricia Ltd)
400 gram (ACBS).NHS indicative price = £ 40. 79
TYR Anamix Infant powder(Nutricia Ltd)
400 gram (ACBS).NHS indicative price = £ 40. 79
TYR Anamix®Junior
▶Nutritional supplement for the dietary management of proven
tyrosinaemia in children 1–10 years.
POWDER, protein equivalent (essential and non-essential amino
acids except phenylalanine and tyrosine) 8.4 g, carbohydrate
11g, fat 3.9 g, energy 475 kJ (113 kcal)/29-g sachet, with
vitamins, minerals, and trace elements.
TYR Anamix Junior oral powder 29g sachets(Nutricia Ltd)
30 sachet (ACBS).NHS indicative price = £ 206. 40
TYR Anamix®Junior LQ
▶Nutritional supplement for the dietary management of
tyrosinaemia type 1 (when nitisinone (NTBC) is used, see
nitisinone p. 612), type II, and type III, in children over 1 year.
LIQUID, protein equivalent (essential and non-essential amino
acids except phenylalanine and tyrosine) 10g,carbohydrate
8.8 g, fat 4.8 g,fibre 310 mg, energy 500 kJ (119 kcal)/125mL,
with vitamins, minerals and trace elements.
TYR Anamix Junior LQ liquid(Nutricia Ltd)
125 ml (ACBS).NHS indicative price = £ 9. 46
TYR cooler® 15
▶Nutritional supplement for the dietary management of
tyrosinaemia in children over 3 years and adults.
LIQUID, protein equivalent (essential and non-essential amino
acids except tyrosine and phenylalanine) 15g, carbohydrate 7 g,
fat 500 mg, energy 393 kJ (92 kcal)/130mL, with vitamins,
minerals, and trace elements.
TYR orange cooler 15 liquid(Vitaflo International Ltd)
130 ml (ACBS).NHS indicative price = £ 11. 87
TYR red cooler 10 liquid(Vitaflo International Ltd)
87 ml (ACBS).NHS indicative price = £ 7. 60
TYR red cooler 15 liquid(Vitaflo International Ltd)
130 ml (ACBS).NHS indicative price = £ 11. 87
TYR red cooler 20 liquid(Vitaflo International Ltd)
174 ml (ACBS).NHS indicative price = £ 15. 89
TYR express15®
▶Nutritional supplement for the dietary management of
tyrosinaemia in children over 8 years and adults.
POWDER, protein equivalent (essential and non-essential amino
acids except tyrosine and phenylalanine) 15g, carbohydrate
3.4 g, fat less than 100 mg, energy 310 kJ (74kcal)/25 g, with
vitamins, minerals, and trace elements. Toflavour unflavoured
products, see FlavourPac p. 1040.
TYR express 15 oral powder 25g sachets(Vitaflo International Ltd)
30 sachet (ACBS).NHS indicative price = £ 349. 27
TYR express20®
▶Nutritional supplement for the dietary management of
tyrosinaemia in children over 8 years.
POWDER, protein equivalent (essential and non-essential amino
acids except tyrosine and phenylalanine) 20g, carbohydrate
4.7 g, fat less than 100 mg, energy 416 kJ (99kcal)/34 g, with
vitamins, minerals, and trace elements. Toflavour unflavoured
products, see FlavourPac p. 1040.
TYR express 20 oral powder 34g sachets(Vitaflo International Ltd)
30 sachet (ACBS).NHS indicative price = £ 451. 25
TYR Gel®
▶Nutritional supplement for the dietary management of
tyrosinaemia in children 1–10 years.
GEL, protein equivalent (essential and non-essential amino
acids except tyrosine and phenylalanine) 10g, carbohydrate
10.3 g, fat less than 100 mg, energy 339 kJ (81 kcal)/24g, with
vitamins, minerals and trace elements. Toflavour unflavoured
products, see FlavourPac p. 1040.
TYR gel oral powder 24g sachets(Vitaflo International Ltd)
30 sachet (ACBS).NHS indicative price = £ 224. 86
TYR Lophlex®LQ 20
▶Nutritional supplement for the dietary management of
tyrosinaemia in children over 3 years and adults.
LIQUID, protein equivalent (essential and non-essential amino
acids except phenylalanine and tyrosine) 20g, carbohydrate
8.8 g, fat less than 500 mg,fibre 500 mg, energy 509 kJ
(120kcal)/125mL, with vitamins, minerals, and trace elements.
TYR Lophlex LQ 20 liquid(Nutricia Ltd)
125 ml (ACBS).NHS indicative price = £ 16. 82BNFC 2018 – 2019 Nutritional supplements for metabolic diseases 1051
Borderline substances|Appendix 2A2