299Prader StageabcNormal I II III IV V NormalTypes of Hypospadias
Glandular
Subcoronal
Distal penile
Midshaft
Proximal penile
PenoscrotalScrotal
PerinealYN YN NormDistalMid
Abd
Abs AbsAbdIng IngL/S^2 L/S^2Prox321000.511.5Labioscrotal
FusionMicro
PhallusUrethral
MeatusRight
GonadLeft
GonadExternal Masculinisation ScoreFig. 9.3 ( a ) Staging to grade the degree of virilization of external genitalia in a 46,XX individual.
( b ) External masculinization score to grade the degree of undervirilization of external genitalia in
a 46,XY individual. ( c ) Grading of hypospadias
features associated with genital ambiguity independently and is more objective.
EMS score for a normal male external genitalia is 12, whereas for a normal
female external genitalia is 0. Both these scores are shown in the fi gure given
below (Fig. 9.3 ).9 Disorders of Sex Development